Lenticonus in spina bifida

Anterior lenticonus is a rare anomaly, first described by Webster (I874), which is frequently associated with Alport's syndrome of nephritis and perceptual deafness. A report of the 42 cases recorded up to I966 is given by Arnott, Crawfurd, and Toghill, i966. South Wales has an unusually high incidence of spina bifida. The incidence was found to be 3-92 per iooo in Glamorgan and Monmouthshire with approximately 30 ooo births per year (Richards and Lowe, 197I). The reason for this is unknown and it was of interest to find a case of spina bifida having anterior lenticonus with other multiple congenital abnormalities.